Anaesthetic and airway management in a child with Hanhart's syndrome

Karakaya D., Baris S., Belet N., Guneren E., Ustun E.

PAEDIATRIC ANAESTHESIA, cilt.13, sa.3, ss.263-266, 2003 (SCI-Expanded) identifier identifier

  • Yayın Türü: Makale / Tam Makale
  • Cilt numarası: 13 Sayı: 3
  • Basım Tarihi: 2003
  • Doi Numarası: 10.1046/j.1460-9592.2003.01029.x
  • Dergi Adı: PAEDIATRIC ANAESTHESIA
  • Derginin Tarandığı İndeksler: Science Citation Index Expanded (SCI-EXPANDED), Scopus
  • Sayfa Sayıları: ss.263-266
  • Anahtar Kelimeler: Hanhart's syndrome, oromandibular-limb hypogenesis syndrome, difficult airway, anaesthetic management, LIMB HYPOGENESIS SYNDROME
  • Ondokuz Mayıs Üniversitesi Adresli: Evet

Özet

Hanhart's syndrome (oromandibular-limb hypogenesis syndrome) is a rare disease characterized by hypoglossia/aglossia, various distal limb defects and micrognathia. Difficult airway due to micrognathia may complicate anaesthetic management in this syndrome. We describe the anaesthetic management of a child with Hanhart's syndrome undergoing plastic reconstructive surgery.