Percutaneous closure of isolated ostium secundum-type atrial septal defect in a patient with Mayer-Rokitansky-Kuster-Hauser syndrome


Akcay M., Gülel O., Soylu K., Meriç M., Elmalı M.

REVISTA PORTUGUESA DE CARDIOLOGIA, cilt.35, sa.12, 2016 (SCI-Expanded) identifier identifier identifier

  • Yayın Türü: Makale / Tam Makale
  • Cilt numarası: 35 Sayı: 12
  • Basım Tarihi: 2016
  • Doi Numarası: 10.1016/j.repc.2016.02.008
  • Dergi Adı: REVISTA PORTUGUESA DE CARDIOLOGIA
  • Derginin Tarandığı İndeksler: Science Citation Index Expanded (SCI-EXPANDED), Scopus
  • Anahtar Kelimeler: Atrial septal defect, Mayer-Rokitansky-Kuster-Hauser syndrome, Percutaneous closure
  • Ondokuz Mayıs Üniversitesi Adresli: Evet

Özet

Mayer-Rokitansky-Kuster-Hauser (MRKH) syndrome is a rare congenital anomaly characterized by complete or partial aplasia of the uterus and the upper part of the vagina. It is reported to be associated with cardiovascular disorders including atrial septal defect, anomalous pulmonary venous return, aortopulmonary window, pulmonary valve stenosis, mitral valve prolapse, tetralogy of Fallot, truncus arteriosus, and patent ductus arteriosus. Herein, for the first time in the medical literature, we present percutaneous closure of an isolated ostium secundum atrial septal defect in this syndrome. (C) 2016 Sociedade Portuguesa de Cardiologia. Published by Elsevier Espana, S.L.U. All rights reserved.