Atıf İçin Kopyala
Elli M., Can Meydan B., Ceyhan M., Pinarli F. G., Dağdemir A., Ayyildiz H. S., ...Daha Fazla
TUMORI JOURNAL, cilt.93, sa.6, ss.641-644, 2007 (SCI-Expanded)
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Yayın Türü:
Makale / Tam Makale
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Cilt numarası:
93
Sayı:
6
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Basım Tarihi:
2007
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Dergi Adı:
TUMORI JOURNAL
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Derginin Tarandığı İndeksler:
Science Citation Index Expanded (SCI-EXPANDED), Scopus
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Sayfa Sayıları:
ss.641-644
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Anahtar Kelimeler:
angiosarcoma, childhood, malignant peripheral nerve sheath tumors, NF1, VASCULAR TUMORS, ANGIOSARCOMA, SARCOMA, ADOLESCENTS, BENIGN
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Ondokuz Mayıs Üniversitesi Adresli:
Evet
Özet
Malignant peripheral nerve sheath tumors (MPNSTs) are uncommon in children and adolescents but occur more frequently in NF1 patients. Angiosarcomatous differentiation in MPNSTs is a rare entity with poor prognosis. We report on a 13-year-old boy with intrathoracic angiosarcoma arising in MPNST associated with NF1.