A Rare Cause of Acute Abdominal Pain Herlyn-Werner-Wunderlich Syndrome

Aydin R., Özdemir A. Z., Ozturk B., Ceyhan Bilgici M. N., TOSUN M.

PEDIATRIC EMERGENCY CARE, cilt.30, sa.1, ss.40-42, 2014 (SCI-Expanded) identifier identifier identifier

  • Yayın Türü: Makale / Tam Makale
  • Cilt numarası: 30 Sayı: 1
  • Basım Tarihi: 2014
  • Doi Numarası: 10.1097/pec.0000000000000052
  • Dergi Adı: PEDIATRIC EMERGENCY CARE
  • Derginin Tarandığı İndeksler: Science Citation Index Expanded (SCI-EXPANDED), Scopus
  • Sayfa Sayıları: ss.40-42
  • Anahtar Kelimeler: mullerian duct anomaly, acute urinary retention, acute abdominal pain, Herlyn-Werner-Wunderlich syndrome, IPSILATERAL RENAL AGENESIS, BLIND HEMIVAGINA, UTERUS, MANAGEMENT
  • Ondokuz Mayıs Üniversitesi Adresli: Evet

Özet

Herlyn-Werner-Wunderlich (HWW) syndrome is a rare mullerian duct anomaly with uterus didelphys, unilateral obstructed hemivagina, and ipsilateral renal agenesis. Patients with this syndrome generally present after menarche with pelvic pain and mass and, rarely, primary infertility in later years. Strong suspicion and knowledge of this syndrome are mandatory for an accurate diagnosis. A 14-year-old female patient presented with acute retention of urine and abdominopelvic pain. Her condition was diagnosed with the use ultrasonography and magnetic resonance imaging as a case of HWW syndrome. She was treated with vaginal hemiseptal resection. The HWW syndrome should be considered among the differential diagnoses in girls with renal anomalies presenting with pelvic mass, symptoms of acute abdominal pain, and acute urinary retention.